Case report Bone marrow transplantation as treatment for X-linked immunodeficiency with hyper-IgM
نویسندگان
چکیده
We report a 10-year-old boy with a severe form of immunodeficiency with hyper-IgM who underwent successful bone marrow transplantation with his HLA-matched sister as donor. Busulfan (20 mg/kg) and cyclophosphamide (200 mg/kg) were used as conditioning. The post-transplant course was uneventful. He is alive 25 months later with full hematological and immunological reconstitution. BORDIGONI, P, et al. Bone marrow transplantation as treatment for X-linked immunodeficiency with hyper-IgM. Bone Marrow Transplantation , 1998, vol. 22, no. 11, p. 1111-4 DOI : 10.1038/sj.bmt.1701497
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